| About the author: |
E. E. Imanov, I. O. Ditkivskyy, O. I. Plyska, O. A. Mazur, A. O. Sloboda, F. Z. Abdullayev |
| Heading |
CLINICAL MEDICINE |
| Type of article |
Scentific article |
| Annotation |
With the purpose to compare in-hospital and late outcomes of endovascular palliation, and surgical interventions in patients with pulmonary artery atresia 138 consecutive patients with the same pathology were analyzed since 2006 (115 patients underwent surgery – 160 surgical procedures, and 23 – underwent 32 endovascular procedures). Long-term outcomes studied on 12 years. The necessity for re-interventions following endovascular, and surgical procedures was analyzed. In surgical group mean length of hospital stay was 26±18.6 days, in endovascular group–22±5.7 days. Rate of surgical and endovascular procedures for pulmonary artery atresia Type I was 53.9 % and 56.5 %, respectively, whereas patients with pulmonary artery atresia Type II: 41.7 % vs.17.4 %, respectively (p<0.001). Patients with Types III and IV predominantly underwent endovascular procedures in 8.7 % and 17.4 %. Endovascular palliation follows with three-fold lower rate of fatal complications vs. surgical interventions: 4.3 % vs. 13 %. Endovascular interventions are choice of option for first stage palliation for infants with pulmonary artery atresia. |
| Tags |
pulmonary artery atresia,endovascular interventions,surgical procedures |
| Bibliography |
- Cantinotti M, McMahon CJ, Marchese P, Köstenberger M, Scalese M, Franchi E, et al. Echocardiographic Parameters for Risk Prediction in Borderline Right Ventricle: Review with Special Emphasis on Pulmonary Atresia with Intact Ventricular Septum and Critical Pulmonary Stenosis. J Clin Med. 2023 Jul 10;12(14):4599. doi: 10.3390/jcm12144599.
- Gorla SR, Singh AP. Pulmonary Atresia With Intact Ventricular Septum. 2024 Jul 27. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2025 Jan–. PMID: 31536272.
- Iliopoulos I, Mastropietro CW, Flores S, Cheung E, Amula V, Radman M, et al. Collaborative Research from the Pediatric Cardiac Intensive Care Society Investigators. Pulmonary Atresia with Intact Ventricular Septum: Midterm Outcomes from a Multicenter Cohort. Pediatr Cardiol. 2024 Apr;45(4):847-857. doi: 10.1007/s00246-022-02954-5.
- LaPar DJ, Bacha E. Pulmonary Atresia With Intact Ventricular Septum With Borderline Tricuspid Valve: How Small Is Too Small. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2019;22:27-31. doi: 10.1053/j.pcsu.2019.02.007.
- Loomba RS, Pelech AN. Aortic perfusion score for pulmonary atresia with intact ventricular septum: An antegrade coronary perfusion scoring system that is predictive of need for transplant and mortality. Congenit Heart Dis. 2018 Jan;13(1):92-97. doi: 10.1111/chd.12510.
- Luo G, Liu A, Sun H, Wang K, Pan S. A case report of pulmonary atresia with intact ventricular septum: an extraordinary finding of subsystemic right ventricle. Front Pediatr. 2024 May 1;12:1251274. doi: 10.3389/fped.2024.1251274.
- Manhem S, Odermarsky M, Wåhlander H, Ekman-Joelsson BM. Pulmonary Atresia with Intact Ventricular Septum, a National Comparison Between Interventional and Surgical Approach, in Combination with a Systemic Literature Review. Pediatr Cardiol. 2024 Jul 5. doi: 10.1007/s00246-024-03566-x.
- Sana MK, Ahmed Z. Pulmonary Atresia With Ventricular Septal Defect. 2024 May 7. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2025 Jan–. PMID: 32965948.
- Vall Camell M, Rodríguez-Fanjul J, Bautista Rodríguez C, Pradda FH, Caffarena-Calvar JM, Iriondo Sanz M, et al. Manejo percutáneo de la atresia pulmonar con tabique interventricular íntegro y la estenosis pulmonar crítica [Percutaneous management of pulmonary atresia with intact ventricular septum and critical pulmonary stenosis]. An Pediatr (Engl Ed). 2019 Nov;91(5):336-343. doi: 10.1016/j.anpedi.2018.10.020. [In Spanish].
- Wolter A, Markert N, Wolter JS, Kurkevych A, Degenhardt J, Ritgen J, et al. Natural history of pulmonary atresia with intact ventricular septum (PAIVS) and critical pulmonary stenosis (CPS) and prediction of outcome. Arch Gynecol Obstet. 2021 Jul;304(1):81-90. doi: 10.1007/s00404-020-05929-0.
- Zhao L, Wang L, Xia H, Wu Y, Jiao X, Zhu H, et al. Prognosis and outcome of intrauterine treatment of fetuses with critical congenital heart disease. Chin Med J (Engl). 2024 Jun 20;137(12):1431-1436. doi: 10.1097/CM9.0000000000002796.
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| Publication of the article |
«World of Medicine and Biology» №1(91), 2025 year, 050-055 pages, index UDK 616.12-007-053.1; 612.171.7 |
| DOI |
10.26724/2079-8334-2025-1-91-50-55 |
